Idiopathic lobular panniculitis (Weber Christian disease): a case report.
نویسندگان
چکیده
Weber Christian disease, an idiopathic relapsing febrile subcutaneous and visceral panniculitis is a rare disease in children. We report a case of Weber Christian disease for he first time from Kanti Children's Hospital.
منابع مشابه
Weber-Christian disease: a case report.
Weber-Christian disease is a rare and poorly understood disorder of the adipose tissue.1,2 The exact aetiopathogenesis of this condition is largely unknown and it is also called idiopathic lobular panniculitis.3 In 1892, Pfeifer first described the skin condition now known as Weber-Christian disease, or idiopathic lobular panniculitis.4,5 In 1925, Weber further depicted the syndrome as case of ...
متن کاملWeber Christian disease.
Weber Christian disease or idiopathic lobular panniculitis is a skin condition that features recurring inflammation in the fat layer of the skin. We report a case of a 17 year old boy with Weber Christian disease as its occurence is extremely rare with only sparse case reports available, who presented with eighteen-month history off fever with chills off and on, arthralgia predominantly of the ...
متن کاملIdiopathic lobular panniculitis with specific pleural involvement.
A 19 year old man presented with fever and left pleural effusion. Biopsy of a subcutaneous nodule and bone marrow led to the diagnosis of idiopathic lobular panniculitis (Weber-Christian disease). Thoracoscopically guided biopsy of the visceral pleura also revealed panniculitis change in the pleural adipose tissue.
متن کاملPfeifer-Weber-Christian Disease during Pregnancy Successfully Treated with Corticosteroids
Sir, Pfeifer–Weber–Christian disease (PWCD), also known as idiopathic relapsing febrile lobular nonsuppurative panniculitis, is a rare inflammatory disorder of subcutaneous adipose tissue.[1] There is no specific test for diagnosis and extensive investigations are required to exclude systemic causes of panniculitis. No uniform effective therapy is available and various drugs have been used in t...
متن کاملIdiopatic lobular necrotizing paniculitis.
42-year old patient was presented to our clinic with a fever lasting for seven months and a ten month history of subcutaneous nodules on all extremities and trunk. Further examination revealed anaemia, lymphocytopenia and elevation of inflammatory parameters and liver enzymes. Authors comment their difficulties in differential diagnostic process. The bone marrow biopsy and reappraisal of subcut...
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ورودعنوان ژورنال:
- Kathmandu University medical journal
دوره 4 2 شماره
صفحات -
تاریخ انتشار 2006